Cor triatriatum is a rare congenital abnormality, causing a cardiac malformation involving the left atrium (cor triatriatum sinister/sinistrum) or, more rarely, the right atrium (cor triatriatum dextra/dextrum) [1]. Anatomical features involve the atrium being divided into two distinct chambers by a thick, fibromuscular septum, with either horizontal or transverse orientation, and which may be band-like or funnel shaped—resulting in three atrial compartments [2]. In the clinical setting, consequences are directly related to the size of the orifice between the true atrial chamber and the accessory chamber. Adults, in most cases, are asymptomatic. Appearance of symptoms are secondary to fibrosis and calcification of the accessory membrane orifice.
Cor Triatriatum Sinister: A Rare Congenital Phenomenon in our Everyday Clinical-Surgical Practice
Lorenzo Giovannico;Domenico Parigino;Tomaso BottioValidation
;Aldo Domenico MilanoConceptualization
2024-01-01
Abstract
Cor triatriatum is a rare congenital abnormality, causing a cardiac malformation involving the left atrium (cor triatriatum sinister/sinistrum) or, more rarely, the right atrium (cor triatriatum dextra/dextrum) [1]. Anatomical features involve the atrium being divided into two distinct chambers by a thick, fibromuscular septum, with either horizontal or transverse orientation, and which may be band-like or funnel shaped—resulting in three atrial compartments [2]. In the clinical setting, consequences are directly related to the size of the orifice between the true atrial chamber and the accessory chamber. Adults, in most cases, are asymptomatic. Appearance of symptoms are secondary to fibrosis and calcification of the accessory membrane orifice.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.