GORGOGLIONE, RUGGIERO
GORGOGLIONE, RUGGIERO
DIPARTIMENTO DI BIOSCIENZE , BIOTECNOLOGIE E AMBIENTE
A Mutation in the Mitochondrial Aspartate/Glutamate Carrier Leads to Intramitochondrial Oxidation and an Inflammatory Myopathy in Dutch Shepherd Dogs
2019-01-01 Diane Shelton, G; Minor, Katie M; Li, Kefeng; Naviaux, Jane C; Monk, Jon; Wang, Lin; Guzik, Elizabeth; Guo, Ling T; Porcelli, Vito; Gorgoglione, Ruggiero; Lasorsa, Massimo; Leegwater, Peter J; Persico, Anthony M; Mickelson, James R; Palmieri, Luigi; Naviaux, Robert K
Cardiolipin fingerprinting of leukocytes by MALDI-TOF/MS as a screening tool for Barth syndrome
2015-01-01 Angelini, Roberto; Lobasso, Simona; Gorgoglione, Ruggiero; Bowron, Ann; Steward, Colin G.; Corcelli, Angela
Deletion of gene coding for mitochondrial citrate carrier in C. elegans impairs the acetylcholine synthesis
2017-01-01 Scarcia, Pasquale; Giuseppina, Zampi; Granafei, Sara; Porcelli, Vito; Gorgoglione, Ruggiero; Ann, Saada; Orly, Elpeleg; Sally, Spendiff; Hanns, Lochmuller; Cataldi, Tommaso; Elia, Di Schiavi; Palmieri, Luigi
Drosophila melanogaster Uncoupling Protein-4A (UCP4A) Catalyzes a Unidirectional Transport of Aspartate
2022-01-01 Lunetti, P.; Gorgoglione, R.; Curcio, R.; Marra, F.; Pignataro, A.; Vozza, A.; Riley, C. L.; Capobianco, L.; Palmieri, L.; Dolce, V.; Fiermonte, G.
FAD/NADH Dependent Oxidoreductases: From Different Amino Acid Sequences to Similar Protein Shapes for Playing an Ancient Function
2019-01-01 Trisolini, Lucia; Gambacorta, Nicola; Gorgoglione, Ruggiero; Montaruli, Michele; Laera, Luna; Colella, Francesco; Volpicella, Mariateresa; De Grassi, Anna; Pierri, Ciro Leonardo
Generation of a Yeast Cell Model Potentially Useful to Identify the Mammalian Mitochondrial N-Acetylglutamate Transporter
2023-01-01 Gorgoglione, Ruggiero; Seccia, Roberta; Ahmed, Amer; Vozza, Angelo; Capobianco, Loredana; Lodi, Alessia; Marra, Federica; Paradies, Eleonora; Palmieri, Luigi; Coppola, Vincenzo; Dolce, Vincenza; Fiermonte, Giuseppe
Glutamine-Derived Aspartate Biosynthesis in Cancer Cells: Role of Mitochondrial Transporters and New Therapeutic Perspectives
2022-01-01 Gorgoglione, R.; Impedovo, V.; Riley, C. L.; Fratantonio, D.; Tiziani, S.; Palmieri, L.; Dolce, V.; Fiermonte, G.
KRAS-regulated glutamine metabolism requires UCP2-mediated aspartate transport to support pancreatic cancer growth
2020-01-01 Raho, S.; Capobianco, L.; Malivindi, R.; Vozza, A.; Piazzolla, C.; De Leonardis, F.; Gorgoglione, R.; Scarcia, P.; Pezzuto, F.; Agrimi, G.; Barile, S. N.; Pisano, I.; Reshkin, S. J.; Greco, M. R.; Cardone, R. A.; Rago, V.; Li, Y.; Marobbio, C. M. T.; Sommergruber, W.; Riley, C. L.; Lasorsa, F. M.; Mills, E.; Vegliante, M. C.; De Benedetto, G. E.; Fratantonio, D.; Palmieri, L.; Dolce, V.; Fiermonte, G.
Mitochondrial carriers of Ustilago maydis and Aspergillus terreus involved in itaconate production: same physiological role but different biochemical features
2020-01-01 Scarcia, Pasquale; Gorgoglione, Ruggiero; Messina, Eugenia; Fiermonte, Giuseppe; Blank, Lars Mathias; Wierckx, Nick; Palmieri, Luigi; Agrimi, Gennaro
Mitochondrial citrate carrier deficiency causes neuromuscular transmission impairment
2017-01-01 Palmieri, Luigi; Scarcia, Pasquale; Zampi, Giuseppina; Porcelli, Vito; Gorgoglione, Ruggiero; Elpeleg, Orly; Spendiff, Sally; Lochmuller, Hanns; Di Schiavi, Elia
Molecular and cellular underpinnings of the neurological phenotypes associated to mitochondrial citrate carrier (SLC25A1) deficiency
2017-01-01 Scarcia, Pasquale; Giuseppina, Zampi; Porcelli, Vito; Gorgoglione, Ruggiero; Ann, Saada; Orly, Elpeleg; Amina, Chaouch; Hanns, Lochmuller; Elia, Di Schiavi; Palmieri, Luigi
Molecular identification and functional characterization of a novel glutamate transporter in yeast and plant mitochondria
2018-01-01 Porcelli, Vito; Vozza, Angelo; Calcagnile, Valeria; Gorgoglione, Ruggiero; Arrigoni, Roberto; Fontanesi, Flavia; Marobbio, Carlo Marya; Castegna, Alessandra; Palmieri, Ferdinando; Palmieri, Luigi
Mutations in SLC25A1, encoding the mitochondrial citrate carrier, cause neuromuscular junction transmission defect
2016-01-01 Scarcia, Pasquale; Zampi, Giuseppina; Porcelli, Vito; Gorgoglione, Ruggiero; Pierri, CIRO LEONARDO; Grassi, Anna De; Sadaa, Ann; Elpeleg, Orly; Chaouch, Amina; Lochmuller, Hanns; Schiavi, Elia Di; Palmieri, Luigi
Personalized Medicine in Mitochondrial Health and Disease: Molecular Basis of Therapeutic Approaches Based on Nutritional Supplements and Their Analogs
2022-01-01 Tragni, Vincenzo; Primiano, Guido; Tummolo, Albina; CAFFERATI BELTRAME, Lucas; LA PIANA, Gianluigi; Sgobba, MARIA NOEMI; Cavalluzzi, MARIA MADDALENA; Paterno, Giulia; Gorgoglione, Ruggiero; Volpicella, Mariateresa; Guerra, Lorenzo; Marzulli, Domenico; Servidei, Serenella; DE GRASSI, Anna; Petrosillo, Giuseppe; Lentini, Giovanni; Pierri, CIRO LEONARDO
Regio- and stereoselective biocatalytic hydration of fatty acids from waste cooking oils en route to hydroxy fatty acids and bio-based polyesters
2023-01-01 Biundo, Antonino; Stamm, Arne; Gorgoglione, Ruggiero; Syrén, Per-Olof; Curia, Silvio; Hauer, Bernhard; Capriati, Vito; Vitale, Paola; Perna, Filippo; Agrimi, Gennaro; Pisano, Isabella
SLC25A10 biallelic mutations in intractable epileptic encephalopathy with complex I deficiency
2018-01-01 Punzi, Giuseppe; Porcelli, Vito; Ruggiu, Matteo; Hossain, Faruk; Menga, Alessio; Scarcia, Pasquale; Castegna, Alessandra; Gorgoglione, Ruggiero; Pierri, Ciro L; Laera, Luna; Lasorsa, Francesco M; Paradies, Eleonora; Pisano, Isabella; Marobbio, Carlo; Lamantea, Eleonora; Ghezzi, Daniele; Tiranti, Valeria; Giannattasio, Sergio; Donati, Maria A; Guerrini, Renzo; Palmieri, Luigi; Palmieri, Ferdinando; De Grassi, Anna
The human uncoupling proteins 5 and 6 (UCP5/SLC25A14 and UCP6/SLC25A30) transport sulfur oxyanions, phosphate and dicarboxylates
2019-01-01 Gorgoglione, R.; Porcelli, V.; Santoro, A.; Daddabbo, L.; Vozza, A.; Monne, M.; Di Noia, M. A.; Palmieri, L.; Fiermonte, G.; Palmieri, F.
Yarrowia lipolytica as a Sustainable Microbial Platform for Circular added value Compounds Production
2021-01-01 Biundo, Antonino; Colacicco, Mattia; Ciliberti, Cosetta; Gorgoglione, Ruggiero; Agrimi, Gennaro; Pisano, Isabella
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
A Mutation in the Mitochondrial Aspartate/Glutamate Carrier Leads to Intramitochondrial Oxidation and an Inflammatory Myopathy in Dutch Shepherd Dogs | 1-gen-2019 | Diane Shelton, G; Minor, Katie M; Li, Kefeng; Naviaux, Jane C; Monk, Jon; Wang, Lin; Guzik, Elizabeth; Guo, Ling T; Porcelli, Vito; Gorgoglione, Ruggiero; Lasorsa, Massimo; Leegwater, Peter J; Persico, Anthony M; Mickelson, James R; Palmieri, Luigi; Naviaux, Robert K | |
Cardiolipin fingerprinting of leukocytes by MALDI-TOF/MS as a screening tool for Barth syndrome | 1-gen-2015 | Angelini, Roberto; Lobasso, Simona; Gorgoglione, Ruggiero; Bowron, Ann; Steward, Colin G.; Corcelli, Angela | |
Deletion of gene coding for mitochondrial citrate carrier in C. elegans impairs the acetylcholine synthesis | 1-gen-2017 | Scarcia, Pasquale; Giuseppina, Zampi; Granafei, Sara; Porcelli, Vito; Gorgoglione, Ruggiero; Ann, Saada; Orly, Elpeleg; Sally, Spendiff; Hanns, Lochmuller; Cataldi, Tommaso; Elia, Di Schiavi; Palmieri, Luigi | |
Drosophila melanogaster Uncoupling Protein-4A (UCP4A) Catalyzes a Unidirectional Transport of Aspartate | 1-gen-2022 | Lunetti, P.; Gorgoglione, R.; Curcio, R.; Marra, F.; Pignataro, A.; Vozza, A.; Riley, C. L.; Capobianco, L.; Palmieri, L.; Dolce, V.; Fiermonte, G. | |
FAD/NADH Dependent Oxidoreductases: From Different Amino Acid Sequences to Similar Protein Shapes for Playing an Ancient Function | 1-gen-2019 | Trisolini, Lucia; Gambacorta, Nicola; Gorgoglione, Ruggiero; Montaruli, Michele; Laera, Luna; Colella, Francesco; Volpicella, Mariateresa; De Grassi, Anna; Pierri, Ciro Leonardo | |
Generation of a Yeast Cell Model Potentially Useful to Identify the Mammalian Mitochondrial N-Acetylglutamate Transporter | 1-gen-2023 | Gorgoglione, Ruggiero; Seccia, Roberta; Ahmed, Amer; Vozza, Angelo; Capobianco, Loredana; Lodi, Alessia; Marra, Federica; Paradies, Eleonora; Palmieri, Luigi; Coppola, Vincenzo; Dolce, Vincenza; Fiermonte, Giuseppe | |
Glutamine-Derived Aspartate Biosynthesis in Cancer Cells: Role of Mitochondrial Transporters and New Therapeutic Perspectives | 1-gen-2022 | Gorgoglione, R.; Impedovo, V.; Riley, C. L.; Fratantonio, D.; Tiziani, S.; Palmieri, L.; Dolce, V.; Fiermonte, G. | |
KRAS-regulated glutamine metabolism requires UCP2-mediated aspartate transport to support pancreatic cancer growth | 1-gen-2020 | Raho, S.; Capobianco, L.; Malivindi, R.; Vozza, A.; Piazzolla, C.; De Leonardis, F.; Gorgoglione, R.; Scarcia, P.; Pezzuto, F.; Agrimi, G.; Barile, S. N.; Pisano, I.; Reshkin, S. J.; Greco, M. R.; Cardone, R. A.; Rago, V.; Li, Y.; Marobbio, C. M. T.; Sommergruber, W.; Riley, C. L.; Lasorsa, F. M.; Mills, E.; Vegliante, M. C.; De Benedetto, G. E.; Fratantonio, D.; Palmieri, L.; Dolce, V.; Fiermonte, G. | |
Mitochondrial carriers of Ustilago maydis and Aspergillus terreus involved in itaconate production: same physiological role but different biochemical features | 1-gen-2020 | Scarcia, Pasquale; Gorgoglione, Ruggiero; Messina, Eugenia; Fiermonte, Giuseppe; Blank, Lars Mathias; Wierckx, Nick; Palmieri, Luigi; Agrimi, Gennaro | |
Mitochondrial citrate carrier deficiency causes neuromuscular transmission impairment | 1-gen-2017 | Palmieri, Luigi; Scarcia, Pasquale; Zampi, Giuseppina; Porcelli, Vito; Gorgoglione, Ruggiero; Elpeleg, Orly; Spendiff, Sally; Lochmuller, Hanns; Di Schiavi, Elia | |
Molecular and cellular underpinnings of the neurological phenotypes associated to mitochondrial citrate carrier (SLC25A1) deficiency | 1-gen-2017 | Scarcia, Pasquale; Giuseppina, Zampi; Porcelli, Vito; Gorgoglione, Ruggiero; Ann, Saada; Orly, Elpeleg; Amina, Chaouch; Hanns, Lochmuller; Elia, Di Schiavi; Palmieri, Luigi | |
Molecular identification and functional characterization of a novel glutamate transporter in yeast and plant mitochondria | 1-gen-2018 | Porcelli, Vito; Vozza, Angelo; Calcagnile, Valeria; Gorgoglione, Ruggiero; Arrigoni, Roberto; Fontanesi, Flavia; Marobbio, Carlo Marya; Castegna, Alessandra; Palmieri, Ferdinando; Palmieri, Luigi | |
Mutations in SLC25A1, encoding the mitochondrial citrate carrier, cause neuromuscular junction transmission defect | 1-gen-2016 | Scarcia, Pasquale; Zampi, Giuseppina; Porcelli, Vito; Gorgoglione, Ruggiero; Pierri, CIRO LEONARDO; Grassi, Anna De; Sadaa, Ann; Elpeleg, Orly; Chaouch, Amina; Lochmuller, Hanns; Schiavi, Elia Di; Palmieri, Luigi | |
Personalized Medicine in Mitochondrial Health and Disease: Molecular Basis of Therapeutic Approaches Based on Nutritional Supplements and Their Analogs | 1-gen-2022 | Tragni, Vincenzo; Primiano, Guido; Tummolo, Albina; CAFFERATI BELTRAME, Lucas; LA PIANA, Gianluigi; Sgobba, MARIA NOEMI; Cavalluzzi, MARIA MADDALENA; Paterno, Giulia; Gorgoglione, Ruggiero; Volpicella, Mariateresa; Guerra, Lorenzo; Marzulli, Domenico; Servidei, Serenella; DE GRASSI, Anna; Petrosillo, Giuseppe; Lentini, Giovanni; Pierri, CIRO LEONARDO | |
Regio- and stereoselective biocatalytic hydration of fatty acids from waste cooking oils en route to hydroxy fatty acids and bio-based polyesters | 1-gen-2023 | Biundo, Antonino; Stamm, Arne; Gorgoglione, Ruggiero; Syrén, Per-Olof; Curia, Silvio; Hauer, Bernhard; Capriati, Vito; Vitale, Paola; Perna, Filippo; Agrimi, Gennaro; Pisano, Isabella | |
SLC25A10 biallelic mutations in intractable epileptic encephalopathy with complex I deficiency | 1-gen-2018 | Punzi, Giuseppe; Porcelli, Vito; Ruggiu, Matteo; Hossain, Faruk; Menga, Alessio; Scarcia, Pasquale; Castegna, Alessandra; Gorgoglione, Ruggiero; Pierri, Ciro L; Laera, Luna; Lasorsa, Francesco M; Paradies, Eleonora; Pisano, Isabella; Marobbio, Carlo; Lamantea, Eleonora; Ghezzi, Daniele; Tiranti, Valeria; Giannattasio, Sergio; Donati, Maria A; Guerrini, Renzo; Palmieri, Luigi; Palmieri, Ferdinando; De Grassi, Anna | |
The human uncoupling proteins 5 and 6 (UCP5/SLC25A14 and UCP6/SLC25A30) transport sulfur oxyanions, phosphate and dicarboxylates | 1-gen-2019 | Gorgoglione, R.; Porcelli, V.; Santoro, A.; Daddabbo, L.; Vozza, A.; Monne, M.; Di Noia, M. A.; Palmieri, L.; Fiermonte, G.; Palmieri, F. | |
Yarrowia lipolytica as a Sustainable Microbial Platform for Circular added value Compounds Production | 1-gen-2021 | Biundo, Antonino; Colacicco, Mattia; Ciliberti, Cosetta; Gorgoglione, Ruggiero; Agrimi, Gennaro; Pisano, Isabella |