BOCCANEGRA, BRIGIDA
BOCCANEGRA, BRIGIDA
DIPARTIMENTO DI FARMACIA-SCIENZE DEL FARMACO
254PActivation of complement cascade may trigger inflammation and fibrosis in Duchenne muscular dystrophy: a preclinical investigation on two murine models
2025-01-01 Boccanegra, Brigida; Tulimiero, Lisamaura; Mantuano, Paola; Lenti, Roberta; Denoyelle, Severine; Marinelli, Manuel; Cappellari, Ornella; De Luca, Annamaria
A two-site collaborative study of electrical impedance myography for evaluation of disease progression in murine Duchenne muscular dystrophy models
2025-01-01 Mantuano, Paola; Van Putten, Maaike; Cobb, Buket Sonbas; Putker, Kayleigh; Boccanegra, Brigida; Tanganyika-de Winter, Christa; Tulimiero, Lisamaura; Schneider, Anne-Fleur; Cappellari, Ornella; Van De Vijver, Davy; Engelbeen, Sarah; Pandeya, Sarbesh; Nagy, Janice A; Rutkove, Seward
BCAAs and Di-Alanine supplementation in the prevention of skeletal muscle atrophy: preclinical evaluation in a murine model of hind limb unloading
2021-01-01 Mantuano, P.; Boccanegra, B.; Bianchini, G.; Conte, E.; De Bellis, M.; Sanarica, F.; Camerino, G. M.; Pierno, S.; Cappellari, O.; Allegretti, M.; Aramini, A.; De Luca, A.
Best reference genes for unbiased normalized transcript expression in normal and dystrophic human cell models of myogenesis
2026-01-01 Quarta, Raffaella; Boccanegra, Brigida; Cristiano, Enrica; Ladisa, Alberto; Conte, Elena; Ohana, Jessica; Mouly, Vincent; De Luca, Annamaria; Hildyard, John; Cappellari, Ornella
Blockers of Skeletal Muscle Nav1.4 Channels: From Therapy of Myotonic Syndrome to Molecular Determinants of Pharmacological Action and Back.
2023-01-01 DE BELLIS, Michela; Boccanegra, Brigida; Cerchiara, ALESSANDRO GIOVANNI; Imbrici, Paola; DE LUCA, Annamaria
Branched-chain amino acid supplementation in a mouse model of ageing: Effects on age-related kidney fibrosis
2025-01-01 Lenti, Roberta; Pontrelli, Paola; Mantuano, Paola; Boccanegra, Brigida; Ladisa, Alberto; Bianchini, Luca; Aramini, Andrea; Liantonio, Antonella; Gesualdo, Loreto; De Bellis, Michela; De Luca, Annamaria
Branched-Chain Amino Acids and Di-Alanine Supplementation in Aged Mice: A Translational Study on Sarcopenia
2023-01-01 Mantuano, P.; Boccanegra, B.; Bianchini, G.; Cappellari, O.; Tulimiero, L.; Conte, E.; Cirmi, S.; Sanarica, F.; De Bellis, M.; Mele, A.; Liantonio, A.; Allegretti, M.; Aramini, A.; De Luca, A.
Cell lines of Duchenne Muscular dystrophy patients shows mutation-dependent delay in myogenic program
2025-01-01 Marinelli, Manuel; Cristiano, Enrica; Quarta, Raffaella; Boccanegra, Brigida; Cerchiara, Alessandro Giovanni; Barile, Simona; Mouly, Vincent; Lasorsa, Massimo; Imbrici, Paola; Cappellari, Ornella; De Luca, Annamaria
Circadian Genes as Exploratory Biomarkers in DMD: Results From Both the mdx Mouse Model and Patients
2021-01-01 Rossi, R.; Falzarano, M. S.; Osman, H.; Armaroli, A.; Scotton, C.; Mantuano, P.; Boccanegra, B.; Cappellari, O.; Schwartz, E.; Yuryev, A.; Mercuri, E.; Bertini, E.; D'Amico, A.; Mora, M.; Johansson, C.; Al-Khalili Szigyarto, C.; De Luca, A.; Ferlini, A.
Dasatinib/HP-β-CD inclusion complex based aqueous formulation as a promising tool for the treatment of paediatric neuromuscular disorders
2019-01-01 Cutrignelli, Annalisa; Sanarica, Francesca; Lopalco, Antonio; Lopedota, Angela; Laquintana, Valentino; Franco, Massimo; Boccanegra, Brigida; Mantuano, Paola; De Luca, Annamaria; Denora, Nunzio
Determination of qPCR reference genes suitable for normalizing gene expression in a novel model of Duchenne muscular dystrophy, the D2-mdx mouse
2024-01-01 Boccanegra, Brigida; Lenti, Roberta; Mantuano, Paola; Conte, Elena; Tulimiero, Lisamaura; Piercy, Richard J.; Cappellari, Ornella; Hildyard, John C. W.; De Luca, Annamaria
Diaphragm‐specific effects of L‐citrulline in mdx mice highlight its potential as adjuvant of standard therapy in Duchenne muscular dystrophy
2026-01-01 Tulimiero, Lisamaura; Boccanegra, Brigida; Mantuano, Paola; Mele, Antonietta; De Bellis, Michela; Lenti, Roberta; Sanarica, Francesca; Cirmi, Santa; Conte, Elena; Cappellari, Ornella; Sherrard, Amber E.; Green, Ardawna; Srinivasa, Mira; Fiorotto, Marta L.; De Luca, Annamaria
Drug repurposing based on integrated in silico and in vitro approach to find a therapy for KCNA2-related disorders
2025-01-01 Marinelli, Manuel; Cerchiara, Alessandro; Tondo, Anna Rita; Arigliano, Claudia; Rubino, Egidio Maria; Trisciuzzi, Daniela; Dinoi, Giorgia; Mele, Antonietta; Boccanegra, Brigida; Siragusa, Lydia; Liantonio, Antonella; De Luca, Annamaria; Nicolotti, Orazio; Imbrici, Paola
Electrical impedance myography as a tool for monitoring disease progression in mouse models of Duchenne Muscular Dystrophy: a longitudinal, multisite study
2025-01-01 Mantuano, Paola; Van Putten, Maaike; Sonbas Cobb, Buket; Putker, Kayleigh; Boccanegra, Brigida; Tanganyika-de Winter, Christa; Tulimiero, Lisamaura; Schneider, Anne-Fleur; Cappellari, Ornella; Van De Vijver, Davy; Engelbeen, Sarah; Pandeya, Sarbesh; Nagy, Janice A.; Rutkove, Seward
Ergogenic effect of bcaas and l-alanine supplementation: Proof-of-concept study in a murine model of physiological exercise
2020-01-01 Mantuano, P.; Bianchini, G.; Cappellari, O.; Boccanegra, B.; Conte, E.; Sanarica, F.; Mele, A.; Camerino, G. M.; Brandolini, L.; Allegretti, M.; De Bellis, M.; Aramini, A.; De Luca, A.
From Symptomatic Therapies to Disease-Modifying Approaches for Neuronal Sodium Channel Disorders
2025-01-01 Dinoi, Giorgia; Canfora, Ileana; D'Agnano, Daniela; Boccanegra, Brigida; Conte, Elena; De Luca, Annamaria; Liantonio, Antonella; Sciruicchio, Vittorio; Imbrici, Paola
Growth hormone secretagogues modulate inflammation and fibrosis in mdx mouse model of Duchenne muscular dystrophy
2023-01-01 Boccanegra, B.; Cappellari, O.; Mantuano, P.; Trisciuzzi, D.; Mele, A.; Tulimiero, L.; De Bellis, M.; Cirmi, S.; Sanarica, F.; Cerchiara, A. G.; Conte, E.; Meanti, R.; Rizzi, L.; Bresciani, E.; Denoyelle, S.; Fehrentz, J. -A.; Cruciani, G.; Nicolotti, O.; Liantonio, A.; Torsello, A.; De Luca, A.
Investigation of genotype-phenotype correlation in 2D cell models of Duchenne muscular dystrophy patients shows mutation-dependent defects in mitochondrial respiration and delay in myogenic program
2025-01-01 Marinelli, Manuel; Cristiano, Enrica; Quarta, Raffaella; Boccanegra, Brigida; Cerchiara, Alessandro Giovanni; Barile, Simona; Mouly, Vincent; Lasorsa, Massimo; Imbrici, Paola; Cappellari, Ornella; De Luca, Annamaria
Ion channels as biomarkers of altered myogenesis in myofiber precursors of Duchenne muscular dystrophy
2024-01-01 Cerchiara, Alessandro Giovanni; Imbrici, Paola; Quarta, Raffaella; Cristiano, Enrica; Boccanegra, Brigida; Caputo, Erika; Wells, Dominic J.; Cappellari, Ornella; De Luca, Annamaria
LKB1 signaling is altered in skeletal muscle of a Duchenne muscular dystrophy mouse model
2023-01-01 Boccanegra, Brigida; Mantuano, Paola; Conte, Elena; Cerchiara, Alessandro Giovanni; Tulimiero, Lisamaura; Quarta, Raffaella; Caputo, Erika; Sanarica, Francesca; Forino, Monica; Spadotto, Valeria; Cappellari, Ornella; Fossati, Gianluca; Steinkühler, Christian; De Luca, Annamaria
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| 254PActivation of complement cascade may trigger inflammation and fibrosis in Duchenne muscular dystrophy: a preclinical investigation on two murine models | 1-gen-2025 | Boccanegra, Brigida; Tulimiero, Lisamaura; Mantuano, Paola; Lenti, Roberta; Denoyelle, Severine; Marinelli, Manuel; Cappellari, Ornella; De Luca, Annamaria | |
| A two-site collaborative study of electrical impedance myography for evaluation of disease progression in murine Duchenne muscular dystrophy models | 1-gen-2025 | Mantuano, Paola; Van Putten, Maaike; Cobb, Buket Sonbas; Putker, Kayleigh; Boccanegra, Brigida; Tanganyika-de Winter, Christa; Tulimiero, Lisamaura; Schneider, Anne-Fleur; Cappellari, Ornella; Van De Vijver, Davy; Engelbeen, Sarah; Pandeya, Sarbesh; Nagy, Janice A; Rutkove, Seward | |
| BCAAs and Di-Alanine supplementation in the prevention of skeletal muscle atrophy: preclinical evaluation in a murine model of hind limb unloading | 1-gen-2021 | Mantuano, P.; Boccanegra, B.; Bianchini, G.; Conte, E.; De Bellis, M.; Sanarica, F.; Camerino, G. M.; Pierno, S.; Cappellari, O.; Allegretti, M.; Aramini, A.; De Luca, A. | |
| Best reference genes for unbiased normalized transcript expression in normal and dystrophic human cell models of myogenesis | 1-gen-2026 | Quarta, Raffaella; Boccanegra, Brigida; Cristiano, Enrica; Ladisa, Alberto; Conte, Elena; Ohana, Jessica; Mouly, Vincent; De Luca, Annamaria; Hildyard, John; Cappellari, Ornella | |
| Blockers of Skeletal Muscle Nav1.4 Channels: From Therapy of Myotonic Syndrome to Molecular Determinants of Pharmacological Action and Back. | 1-gen-2023 | DE BELLIS, Michela; Boccanegra, Brigida; Cerchiara, ALESSANDRO GIOVANNI; Imbrici, Paola; DE LUCA, Annamaria | |
| Branched-chain amino acid supplementation in a mouse model of ageing: Effects on age-related kidney fibrosis | 1-gen-2025 | Lenti, Roberta; Pontrelli, Paola; Mantuano, Paola; Boccanegra, Brigida; Ladisa, Alberto; Bianchini, Luca; Aramini, Andrea; Liantonio, Antonella; Gesualdo, Loreto; De Bellis, Michela; De Luca, Annamaria | |
| Branched-Chain Amino Acids and Di-Alanine Supplementation in Aged Mice: A Translational Study on Sarcopenia | 1-gen-2023 | Mantuano, P.; Boccanegra, B.; Bianchini, G.; Cappellari, O.; Tulimiero, L.; Conte, E.; Cirmi, S.; Sanarica, F.; De Bellis, M.; Mele, A.; Liantonio, A.; Allegretti, M.; Aramini, A.; De Luca, A. | |
| Cell lines of Duchenne Muscular dystrophy patients shows mutation-dependent delay in myogenic program | 1-gen-2025 | Marinelli, Manuel; Cristiano, Enrica; Quarta, Raffaella; Boccanegra, Brigida; Cerchiara, Alessandro Giovanni; Barile, Simona; Mouly, Vincent; Lasorsa, Massimo; Imbrici, Paola; Cappellari, Ornella; De Luca, Annamaria | |
| Circadian Genes as Exploratory Biomarkers in DMD: Results From Both the mdx Mouse Model and Patients | 1-gen-2021 | Rossi, R.; Falzarano, M. S.; Osman, H.; Armaroli, A.; Scotton, C.; Mantuano, P.; Boccanegra, B.; Cappellari, O.; Schwartz, E.; Yuryev, A.; Mercuri, E.; Bertini, E.; D'Amico, A.; Mora, M.; Johansson, C.; Al-Khalili Szigyarto, C.; De Luca, A.; Ferlini, A. | |
| Dasatinib/HP-β-CD inclusion complex based aqueous formulation as a promising tool for the treatment of paediatric neuromuscular disorders | 1-gen-2019 | Cutrignelli, Annalisa; Sanarica, Francesca; Lopalco, Antonio; Lopedota, Angela; Laquintana, Valentino; Franco, Massimo; Boccanegra, Brigida; Mantuano, Paola; De Luca, Annamaria; Denora, Nunzio | |
| Determination of qPCR reference genes suitable for normalizing gene expression in a novel model of Duchenne muscular dystrophy, the D2-mdx mouse | 1-gen-2024 | Boccanegra, Brigida; Lenti, Roberta; Mantuano, Paola; Conte, Elena; Tulimiero, Lisamaura; Piercy, Richard J.; Cappellari, Ornella; Hildyard, John C. W.; De Luca, Annamaria | |
| Diaphragm‐specific effects of L‐citrulline in mdx mice highlight its potential as adjuvant of standard therapy in Duchenne muscular dystrophy | 1-gen-2026 | Tulimiero, Lisamaura; Boccanegra, Brigida; Mantuano, Paola; Mele, Antonietta; De Bellis, Michela; Lenti, Roberta; Sanarica, Francesca; Cirmi, Santa; Conte, Elena; Cappellari, Ornella; Sherrard, Amber E.; Green, Ardawna; Srinivasa, Mira; Fiorotto, Marta L.; De Luca, Annamaria | |
| Drug repurposing based on integrated in silico and in vitro approach to find a therapy for KCNA2-related disorders | 1-gen-2025 | Marinelli, Manuel; Cerchiara, Alessandro; Tondo, Anna Rita; Arigliano, Claudia; Rubino, Egidio Maria; Trisciuzzi, Daniela; Dinoi, Giorgia; Mele, Antonietta; Boccanegra, Brigida; Siragusa, Lydia; Liantonio, Antonella; De Luca, Annamaria; Nicolotti, Orazio; Imbrici, Paola | |
| Electrical impedance myography as a tool for monitoring disease progression in mouse models of Duchenne Muscular Dystrophy: a longitudinal, multisite study | 1-gen-2025 | Mantuano, Paola; Van Putten, Maaike; Sonbas Cobb, Buket; Putker, Kayleigh; Boccanegra, Brigida; Tanganyika-de Winter, Christa; Tulimiero, Lisamaura; Schneider, Anne-Fleur; Cappellari, Ornella; Van De Vijver, Davy; Engelbeen, Sarah; Pandeya, Sarbesh; Nagy, Janice A.; Rutkove, Seward | |
| Ergogenic effect of bcaas and l-alanine supplementation: Proof-of-concept study in a murine model of physiological exercise | 1-gen-2020 | Mantuano, P.; Bianchini, G.; Cappellari, O.; Boccanegra, B.; Conte, E.; Sanarica, F.; Mele, A.; Camerino, G. M.; Brandolini, L.; Allegretti, M.; De Bellis, M.; Aramini, A.; De Luca, A. | |
| From Symptomatic Therapies to Disease-Modifying Approaches for Neuronal Sodium Channel Disorders | 1-gen-2025 | Dinoi, Giorgia; Canfora, Ileana; D'Agnano, Daniela; Boccanegra, Brigida; Conte, Elena; De Luca, Annamaria; Liantonio, Antonella; Sciruicchio, Vittorio; Imbrici, Paola | |
| Growth hormone secretagogues modulate inflammation and fibrosis in mdx mouse model of Duchenne muscular dystrophy | 1-gen-2023 | Boccanegra, B.; Cappellari, O.; Mantuano, P.; Trisciuzzi, D.; Mele, A.; Tulimiero, L.; De Bellis, M.; Cirmi, S.; Sanarica, F.; Cerchiara, A. G.; Conte, E.; Meanti, R.; Rizzi, L.; Bresciani, E.; Denoyelle, S.; Fehrentz, J. -A.; Cruciani, G.; Nicolotti, O.; Liantonio, A.; Torsello, A.; De Luca, A. | |
| Investigation of genotype-phenotype correlation in 2D cell models of Duchenne muscular dystrophy patients shows mutation-dependent defects in mitochondrial respiration and delay in myogenic program | 1-gen-2025 | Marinelli, Manuel; Cristiano, Enrica; Quarta, Raffaella; Boccanegra, Brigida; Cerchiara, Alessandro Giovanni; Barile, Simona; Mouly, Vincent; Lasorsa, Massimo; Imbrici, Paola; Cappellari, Ornella; De Luca, Annamaria | |
| Ion channels as biomarkers of altered myogenesis in myofiber precursors of Duchenne muscular dystrophy | 1-gen-2024 | Cerchiara, Alessandro Giovanni; Imbrici, Paola; Quarta, Raffaella; Cristiano, Enrica; Boccanegra, Brigida; Caputo, Erika; Wells, Dominic J.; Cappellari, Ornella; De Luca, Annamaria | |
| LKB1 signaling is altered in skeletal muscle of a Duchenne muscular dystrophy mouse model | 1-gen-2023 | Boccanegra, Brigida; Mantuano, Paola; Conte, Elena; Cerchiara, Alessandro Giovanni; Tulimiero, Lisamaura; Quarta, Raffaella; Caputo, Erika; Sanarica, Francesca; Forino, Monica; Spadotto, Valeria; Cappellari, Ornella; Fossati, Gianluca; Steinkühler, Christian; De Luca, Annamaria |