Sfoglia per Autore
The biochemical properties of the mitochondrial thiamine pyrophosphate carrier from Drosophila melanogaster
2010-01-01 Iacopetta, D; Carrisi, C; DE FILIPPIS, G; Calcagnile, Vm; Cappello, Ar; Chimento, A; Curcio, R; Santoro, A; Vozza, Angelo; Dolce, V; Palmieri, F; Capobianco, L.
A new Caucasian case of neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD): A clinical, molecular, and functional study
2011-01-01 Fiermonte, Giuseppe; Parisi, G; Martinelli, D; DE LEONARDIS, F; Torre, G; Pierri, CIRO LEONARDO; Saccari, A; Lasorsa, Fm; Vozza, Angelo; Palmieri, F; DIONISI VICI, C.
A CLINICAL, MOLECULAR AND FUNCTIONAL STUDY OF A CAUCASIAN CASE OF NEONATAL INTRAHEPATIC CHOLESTASIS CAUSED BY CITRIN DEFICIENCY (NICCD)
2012-01-01 Parisi, G.; Fiermonte, C. L.; Martinelli, D.; De Leonardis, F.; Torre, G.; Pierri, CIRO LEONARDO; Saccari, A.; Lasorsa, F. M.; Vozza, Angelo; Palmieri, F.; Dionisi Vici, F.
UCP2 exports C4 metabolites out of mitochondria in exchange for phosphate.
2014-01-01 Fiermonte, Giuseppe; Vozza, Angelo; Parisi, G.; De Leonardis, F.; Lasorsa, F. M.; Castegna, Alessandra; Amorese, D.; Palmieri, Luigi; Ricquier, D.; Paradies, E.; Scarcia, Pasquale; Palmieri, F.; Bouillaud, F.
Riboflavin responsive mitochondrial myopathy is a new phenotype of dihydrolipoamide dehydrogenase deficiency. The chaperon-like effect of vitamin B2.
2014-01-01 Carrozzo, R; Torraco, A; Fiermonte, Giuseppe; Martinelli, D; Di Nottia, M; Rizza, T; Vozza, Angelo; Verrigni, D; Diodato, D; Parisi, G; Maiorana, A; Rizzo, C; Pierri, CIRO LEONARDO; Zucano, S; Piemonte, F; Bertini, E; Dionisi Vici, C.
Overexpression in E. coli and Purification of the L. pneumophila Lpp2981 Protein.
2014-01-01 Giannuzzi, G.; Lobefaro, N.; Paradies, E.; Vozza, Angelo; Punzi, G.; Marobbio, CARLO MARYA
UCP2 transports C4 metabolites out of mitochondria, regulating glucose and glutamine oxidation
2014-01-01 Vozza, Angelo; Parisi, Giovanni; DE LEONARDIS, Francesco; Lasorsa, Francesco Massimo; Castegna, Alessandra; Amorese, Daniela; Marmo, Raffaele; Calcagnile, VALERIA MARIAJOLANDA; Palmieri, Luigi; Ricquier, Daniel; Paradies, Eleonora; Scarcia, Pasquale; Palmieri, Ferdinando; Bouillaud, Frédéric; Fiermonte, Giuseppe
Unidirectional transport of the mitochondrial GTP/GDP carrier in Saccharomyces cerevisiae
2015-01-01 VILLALOBOS COA, VALENTINA LOIRA; Marobbio, CARLO MARYA; Ventrella, Angela; Li, Yuan; Vozza, Angelo
Functional characterization and organ distribution of three mitochondrial ATP-Mg/Pi carriers in Arabidopsis thaliana
2015-01-01 Monné, Magnus; Miniero, DANIELA VALERIA; Obata, Toshihiro; Daddabbo, Lucia; Palmieri, Luigi; Vozza, Angelo; Nicolardi, M. Cristina; Fernie, Alisdair R.; Palmieri, Ferdinando
New insights about the structural rearrangements required for substrate translocation in the bovine mitochondrial oxoglutarate carrier
2016-01-01 Curcio, Rosita; Muto, Luigina; Pierri, CIRO LEONARDO; Montalto, Anna; Lauria, Graziantonio; Onofrio, Angelo; Fiorillo, Marco; Fiermonte, Giuseppe; Lunetti, Paola; Vozza, Angelo; Capobianco, Loredana; Cappello, Anna Rita; Dolce, Vincenza
Biochemical characterization of a new mitochondrial transporter of dephosphocoenzyme A in Drosophila melanogaster
2016-01-01 Vozza, Angelo; DE LEONARDIS, Francesco; Paradies, Eleonora; DE GRASSI, Anna; Pierri, CIRO LEONARDO; Parisi, Giovanni; Marobbio, CARLO MARYA; Lasorsa, Francesco Massimo; Muto, Luigina; Capobianco, Loredana; Dolce, Vincenza; Raho, Susanna; Fiermonte, Giuseppe
Novel mutations in IBA57 are associated with leukodystrophy and variable clinical phenotypes
2017-01-01 Torraco, Alessandra; Ardissone, Anna; Invernizzi, Federica; Rizza, Teresa; Fiermonte, Giuseppe; Niceta, Marcello; Zanetti, Nadia; Martinelli, Diego; Vozza, Angelo; Verrigni, Daniela; Di Nottia, Michela; Lamantea, Eleonora; Diodato, Daria; Tartaglia, Marco; Dionisi Vici, Carlo; Moroni, Isabella; Farina, Laura; Bertini, Enrico; Ghezzi, Daniele; Carrozzo, Rosalba
Molecular identification and functional characterization of a novel glutamate transporter in yeast and plant mitochondria
2018-01-01 Porcelli, Vito; Vozza, Angelo; Calcagnile, Valeria; Gorgoglione, Ruggiero; Arrigoni, Roberto; Fontanesi, Flavia; Marobbio, Carlo Marya; Castegna, Alessandra; Palmieri, Ferdinando; Palmieri, Luigi
Effect Of Diazoxide on Friedreich Ataxia Models
2018-01-01 Santoro, Antonella; Anjomani Virmouni, Sara; Paradies, Eleonora; Villalobos Coa, Valentina L; Al-Mahdawi, Sahar; Khoo, Mee; Porcelli, Vito; Vozza, Angelo; Perrone, Mara; Denora, Nunzio; Taroni, Franco; Merla, Giuseppe; Palmieri, Luigi; Pook, Mark A; Marobbio, Carlo
ISCA1 mutation in a patient with infantile-onset leukodystrophy causes defects in mitochondrial [4Fe-4S] proteins
2018-01-01 Torraco, Alessandra; Stehling, Oliver; Stümpfig, Claudia; Rösser, Ralf; De Rasmo, Domenico; Fiermonte, Giuseppe; Verrigni, Daniela; Rizza, Teresa; Vozza, Angelo; Di Nottia, Michela; Diodato, Daria; Martinelli, Diego; Piemonte, Fiorella; Dionisi-Vici, Carlo; Bertini, Enrico; Lill, Roland; Carrozzo, Rosalba
The human uncoupling proteins 5 and 6 (UCP5/SLC25A14 and UCP6/SLC25A30) transport sulfur oxyanions, phosphate and dicarboxylates
2019-01-01 Gorgoglione, R.; Porcelli, V.; Santoro, A.; Daddabbo, L.; Vozza, A.; Monne, M.; Di Noia, M. A.; Palmieri, L.; Fiermonte, G.; Palmieri, F.
Mitochondrial Carriers for Aspartate, Glutamate and Other Amino Acids: A Review
2019-01-01 Monne, M.; Vozza, A.; Lasorsa, F. M.; Porcelli, V.; Palmieri, F.
Cloning, Purification, and Characterization of the Catalytic C-Terminal Domain of the Human 3-Hydroxy-3-methyl glutaryl-CoA Reductase: An Effective, Fast, and Easy Method for Testing Hypocholesterolemic Compounds
2020-01-01 Curcio, Rosita; Aiello, Donatella; Vozza, Angelo; Muto, Luigina; Martello, Emanuela; Cappello, Anna Rita; Capobianco, Loredana; Fiermonte, Giuseppe; Siciliano, Carlo; Napoli, Anna; Dolce, Vincenza
KRAS-regulated glutamine metabolism requires UCP2-mediated aspartate transport to support pancreatic cancer growth
2020-01-01 Raho, S.; Capobianco, L.; Malivindi, R.; Vozza, A.; Piazzolla, C.; De Leonardis, F.; Gorgoglione, R.; Scarcia, P.; Pezzuto, F.; Agrimi, G.; Barile, S. N.; Pisano, I.; Reshkin, S. J.; Greco, M. R.; Cardone, R. A.; Rago, V.; Li, Y.; Marobbio, C. M. T.; Sommergruber, W.; Riley, C. L.; Lasorsa, F. M.; Mills, E.; Vegliante, M. C.; De Benedetto, G. E.; Fratantonio, D.; Palmieri, L.; Dolce, V.; Fiermonte, G.
Drosophila melanogaster Uncoupling Protein-4A (UCP4A) Catalyzes a Unidirectional Transport of Aspartate
2022-01-01 Lunetti, P.; Gorgoglione, R.; Curcio, R.; Marra, F.; Pignataro, A.; Vozza, A.; Riley, C. L.; Capobianco, L.; Palmieri, L.; Dolce, V.; Fiermonte, G.
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
The biochemical properties of the mitochondrial thiamine pyrophosphate carrier from Drosophila melanogaster | 1-gen-2010 | Iacopetta, D; Carrisi, C; DE FILIPPIS, G; Calcagnile, Vm; Cappello, Ar; Chimento, A; Curcio, R; Santoro, A; Vozza, Angelo; Dolce, V; Palmieri, F; Capobianco, L. | |
A new Caucasian case of neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD): A clinical, molecular, and functional study | 1-gen-2011 | Fiermonte, Giuseppe; Parisi, G; Martinelli, D; DE LEONARDIS, F; Torre, G; Pierri, CIRO LEONARDO; Saccari, A; Lasorsa, Fm; Vozza, Angelo; Palmieri, F; DIONISI VICI, C. | |
A CLINICAL, MOLECULAR AND FUNCTIONAL STUDY OF A CAUCASIAN CASE OF NEONATAL INTRAHEPATIC CHOLESTASIS CAUSED BY CITRIN DEFICIENCY (NICCD) | 1-gen-2012 | Parisi, G.; Fiermonte, C. L.; Martinelli, D.; De Leonardis, F.; Torre, G.; Pierri, CIRO LEONARDO; Saccari, A.; Lasorsa, F. M.; Vozza, Angelo; Palmieri, F.; Dionisi Vici, F. | |
UCP2 exports C4 metabolites out of mitochondria in exchange for phosphate. | 1-gen-2014 | Fiermonte, Giuseppe; Vozza, Angelo; Parisi, G.; De Leonardis, F.; Lasorsa, F. M.; Castegna, Alessandra; Amorese, D.; Palmieri, Luigi; Ricquier, D.; Paradies, E.; Scarcia, Pasquale; Palmieri, F.; Bouillaud, F. | |
Riboflavin responsive mitochondrial myopathy is a new phenotype of dihydrolipoamide dehydrogenase deficiency. The chaperon-like effect of vitamin B2. | 1-gen-2014 | Carrozzo, R; Torraco, A; Fiermonte, Giuseppe; Martinelli, D; Di Nottia, M; Rizza, T; Vozza, Angelo; Verrigni, D; Diodato, D; Parisi, G; Maiorana, A; Rizzo, C; Pierri, CIRO LEONARDO; Zucano, S; Piemonte, F; Bertini, E; Dionisi Vici, C. | |
Overexpression in E. coli and Purification of the L. pneumophila Lpp2981 Protein. | 1-gen-2014 | Giannuzzi, G.; Lobefaro, N.; Paradies, E.; Vozza, Angelo; Punzi, G.; Marobbio, CARLO MARYA | |
UCP2 transports C4 metabolites out of mitochondria, regulating glucose and glutamine oxidation | 1-gen-2014 | Vozza, Angelo; Parisi, Giovanni; DE LEONARDIS, Francesco; Lasorsa, Francesco Massimo; Castegna, Alessandra; Amorese, Daniela; Marmo, Raffaele; Calcagnile, VALERIA MARIAJOLANDA; Palmieri, Luigi; Ricquier, Daniel; Paradies, Eleonora; Scarcia, Pasquale; Palmieri, Ferdinando; Bouillaud, Frédéric; Fiermonte, Giuseppe | |
Unidirectional transport of the mitochondrial GTP/GDP carrier in Saccharomyces cerevisiae | 1-gen-2015 | VILLALOBOS COA, VALENTINA LOIRA; Marobbio, CARLO MARYA; Ventrella, Angela; Li, Yuan; Vozza, Angelo | |
Functional characterization and organ distribution of three mitochondrial ATP-Mg/Pi carriers in Arabidopsis thaliana | 1-gen-2015 | Monné, Magnus; Miniero, DANIELA VALERIA; Obata, Toshihiro; Daddabbo, Lucia; Palmieri, Luigi; Vozza, Angelo; Nicolardi, M. Cristina; Fernie, Alisdair R.; Palmieri, Ferdinando | |
New insights about the structural rearrangements required for substrate translocation in the bovine mitochondrial oxoglutarate carrier | 1-gen-2016 | Curcio, Rosita; Muto, Luigina; Pierri, CIRO LEONARDO; Montalto, Anna; Lauria, Graziantonio; Onofrio, Angelo; Fiorillo, Marco; Fiermonte, Giuseppe; Lunetti, Paola; Vozza, Angelo; Capobianco, Loredana; Cappello, Anna Rita; Dolce, Vincenza | |
Biochemical characterization of a new mitochondrial transporter of dephosphocoenzyme A in Drosophila melanogaster | 1-gen-2016 | Vozza, Angelo; DE LEONARDIS, Francesco; Paradies, Eleonora; DE GRASSI, Anna; Pierri, CIRO LEONARDO; Parisi, Giovanni; Marobbio, CARLO MARYA; Lasorsa, Francesco Massimo; Muto, Luigina; Capobianco, Loredana; Dolce, Vincenza; Raho, Susanna; Fiermonte, Giuseppe | |
Novel mutations in IBA57 are associated with leukodystrophy and variable clinical phenotypes | 1-gen-2017 | Torraco, Alessandra; Ardissone, Anna; Invernizzi, Federica; Rizza, Teresa; Fiermonte, Giuseppe; Niceta, Marcello; Zanetti, Nadia; Martinelli, Diego; Vozza, Angelo; Verrigni, Daniela; Di Nottia, Michela; Lamantea, Eleonora; Diodato, Daria; Tartaglia, Marco; Dionisi Vici, Carlo; Moroni, Isabella; Farina, Laura; Bertini, Enrico; Ghezzi, Daniele; Carrozzo, Rosalba | |
Molecular identification and functional characterization of a novel glutamate transporter in yeast and plant mitochondria | 1-gen-2018 | Porcelli, Vito; Vozza, Angelo; Calcagnile, Valeria; Gorgoglione, Ruggiero; Arrigoni, Roberto; Fontanesi, Flavia; Marobbio, Carlo Marya; Castegna, Alessandra; Palmieri, Ferdinando; Palmieri, Luigi | |
Effect Of Diazoxide on Friedreich Ataxia Models | 1-gen-2018 | Santoro, Antonella; Anjomani Virmouni, Sara; Paradies, Eleonora; Villalobos Coa, Valentina L; Al-Mahdawi, Sahar; Khoo, Mee; Porcelli, Vito; Vozza, Angelo; Perrone, Mara; Denora, Nunzio; Taroni, Franco; Merla, Giuseppe; Palmieri, Luigi; Pook, Mark A; Marobbio, Carlo | |
ISCA1 mutation in a patient with infantile-onset leukodystrophy causes defects in mitochondrial [4Fe-4S] proteins | 1-gen-2018 | Torraco, Alessandra; Stehling, Oliver; Stümpfig, Claudia; Rösser, Ralf; De Rasmo, Domenico; Fiermonte, Giuseppe; Verrigni, Daniela; Rizza, Teresa; Vozza, Angelo; Di Nottia, Michela; Diodato, Daria; Martinelli, Diego; Piemonte, Fiorella; Dionisi-Vici, Carlo; Bertini, Enrico; Lill, Roland; Carrozzo, Rosalba | |
The human uncoupling proteins 5 and 6 (UCP5/SLC25A14 and UCP6/SLC25A30) transport sulfur oxyanions, phosphate and dicarboxylates | 1-gen-2019 | Gorgoglione, R.; Porcelli, V.; Santoro, A.; Daddabbo, L.; Vozza, A.; Monne, M.; Di Noia, M. A.; Palmieri, L.; Fiermonte, G.; Palmieri, F. | |
Mitochondrial Carriers for Aspartate, Glutamate and Other Amino Acids: A Review | 1-gen-2019 | Monne, M.; Vozza, A.; Lasorsa, F. M.; Porcelli, V.; Palmieri, F. | |
Cloning, Purification, and Characterization of the Catalytic C-Terminal Domain of the Human 3-Hydroxy-3-methyl glutaryl-CoA Reductase: An Effective, Fast, and Easy Method for Testing Hypocholesterolemic Compounds | 1-gen-2020 | Curcio, Rosita; Aiello, Donatella; Vozza, Angelo; Muto, Luigina; Martello, Emanuela; Cappello, Anna Rita; Capobianco, Loredana; Fiermonte, Giuseppe; Siciliano, Carlo; Napoli, Anna; Dolce, Vincenza | |
KRAS-regulated glutamine metabolism requires UCP2-mediated aspartate transport to support pancreatic cancer growth | 1-gen-2020 | Raho, S.; Capobianco, L.; Malivindi, R.; Vozza, A.; Piazzolla, C.; De Leonardis, F.; Gorgoglione, R.; Scarcia, P.; Pezzuto, F.; Agrimi, G.; Barile, S. N.; Pisano, I.; Reshkin, S. J.; Greco, M. R.; Cardone, R. A.; Rago, V.; Li, Y.; Marobbio, C. M. T.; Sommergruber, W.; Riley, C. L.; Lasorsa, F. M.; Mills, E.; Vegliante, M. C.; De Benedetto, G. E.; Fratantonio, D.; Palmieri, L.; Dolce, V.; Fiermonte, G. | |
Drosophila melanogaster Uncoupling Protein-4A (UCP4A) Catalyzes a Unidirectional Transport of Aspartate | 1-gen-2022 | Lunetti, P.; Gorgoglione, R.; Curcio, R.; Marra, F.; Pignataro, A.; Vozza, A.; Riley, C. L.; Capobianco, L.; Palmieri, L.; Dolce, V.; Fiermonte, G. |
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